Ramsay Hunt Syndrome Type 2

Ramsay Hunt syndrome type 2 is also called dyssynergia cerebellaris myoclonica. It refers to a collection of neurological disorders. These are both rare and degenerative. It is characterized by:

  • Epilepsy.

  • Cognitive impairment.

  • Myoclonus.

  • Progressive ataxia.

Some cases are due to mitochondrial abnormalities.

SYMPTOMS

Symptoms include:

  • Seizures.

  • Tremor.

  • Reduced muscle coordination.

Onset of the disorder generally occurs in early adulthood. Tremor may begin in one extremity. Later it may spread to involve the entire voluntary muscular system. Arms are usually more affected than legs.

TREATMENT

Treatment of Ramsay Hunt type 2 is symptomatic. Myoclonus and seizures may be treated with drugs like valproate.The progression of the disorder is usually 10 years or longer.